Pesquisa sobre: GAMMA-BUTYROBETAINE DIOXYGENASE 
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Descritor Inglês:   gamma-Butyrobetaine Dioxygenase 
Descritor Espanhol:   gamma-Butirobetaína Dioxigenasa 
Descritor Português:   gama-Butirobetaína Dioxigenase 
Categoria:   D08.811.682.690.708.401
Definição Inglês:   An enzyme that catalyzes the HYDROXYLATION of gamma-butyrobetaine to L-CARNITINE. It is the last enzyme in the biosynthetic pathway of L-CARNITINE and is dependent on alpha-ketoglutarate; IRON; ASCORBIC ACID; and OXYGEN. 
Nota Histórica Inglês:   2006(1980); use KETOGLUTARIC ACID 1973-1974, BETAINE 1972-1979, BUTYRATES 1974-1979, & AMINOBUTYRIC ACID 1970-1974 
Qualificadores Permitidos Inglês:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DF deficiency
DE drug effects EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
SE secretion ST standards
SD supply & distribution TU therapeutic use
TO toxicity UL ultrastructure
UR urine  
Número do Registro:   50661 
Identificador Único:   D050563 

Ocorrência na BVS:
 

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